Shamsa A, Parizadeh M, Asle Zareh M, Movarrekh M. Aphallia with urethrorectal fistula, bladder and urethral calculi . J Shahid Sadoughi Univ Med Sci Health Serv. 2006; 14 (1) :77-80
URL:
http://jssu.ssu.ac.ir/article-1-752-en.html
Abstract: (11745 Views)
Introduction: Aphallia is a very rare urogenital anomaly with incidence rate of 1 in 30,000,000. It usually coexists with other anomalies such as cardiovascular anomalies which are incompatible with normal life, and therefore infants are delivered stillbirth or live for a very short period of time.
Methods: We present an 18 months old boy with aphallia associated with congenital urethrorectal fistula, bladder and urethral stones. All stones were removed endourologically, recto-urethral fistula was repaired and perincal urethrostomy was performed.
Results: The stones were composed of calcium phosphate colonized by klebiella pneumonia and proteus mirabilis. Urethrorectal fistula repairment was confirmed by cystography. Patient was discharged without a urinary catheter.
Conclusion: In developed countries, management of such patients is to raise them as females. However, we must consider socio-cultural conditions, parents preference and patients tendency in management of aphallia.
Type of Study:
Original article |
Subject:
General Received: 2010/01/25 | Published: 2006/04/15